선천 눈확뇌탈출, 눈확위치이상, 안구돌출증 증례보고

초록

Purpose:We present here an excoodingly rare variant of a non-midline basal encephalocele of the spheno-orbital type, and this was accompanied with orbital dystopia in a 56-year-old man. Methods: On exam, his left eye was located more infero-laterally than his right eye and the pa-tient said this had been this way since his birth. The prothusion of his left eye was aggravated when he is tired. His naked visual acuity was 0.7/0.3,and the ocular pressure was 14mmHg/12mmHg. The exopthalmometry was 10mm/14-16mm. His eyeball motion was not restrocted, yet diplopia was present in all directions. The distance from the midline to the medial canthus was 20mm/15mm. The distance form the midline to the midpupillary line was 35mm/22mm. The vertical dimension of the palpebral fissure was 12mm/9mm. The height difference of the upper eyelid margin was 11mm,and the height duifference of the lower eyelid mar-gin was 8mm. Results: Facial CTand MRI showed left sphe-noid wing hypoplasia and herniation of the left an-terior temporal pole and dura mater into the orbit,and this resulted left exophtalmus and ence-phalomalaia in the left anterior temporal pole. Conclusion: To the best of our knowledge, our case is the second case of basal encephalocele and orbital dystopia.