acylcarnitine Profile과 DNA 분석을 이용하여 MTP 결핍증으로 진단된 남자환아 1 례

The first case of mitochondrial trifunctional protein deficiency diagnosed by acylcarnitine profile and DNA analysis in a dried blood spot of 4 day- old Korean baby boy

초록

Summary : We report here the first Korean case with TFP deficiency, whose molecular diagnosis revealed a novel mutation in the ?subunit of the TFP and the rare combination of two intergenic region (C/C and G/G) polymorphisms.

제목
acylcarnitine Profile과 DNA 분석을 이용하여 MTP 결핍증으로 진단된 남자환아 1 례
제목 (타언어)
The first case of mitochondrial trifunctional protein deficiency diagnosed by acylcarnitine profile and DNA analysis in a dried blood spot of 4 day- old Korean baby boy
저자
LEE JI EUN
학회명
제3회 대한 유전성 대사 질환 학회