Hirayama Disease with Proximal Upper Extremity Atrophy mimicking brachial plexopathy

초록

Hirayama disease is characterized by progressive muscular weakness and wasting of unilateral forearms and hands in young people. The hypothesis is based on chronic ischemic damage to the lower cervical cord caused by crushing against the vertebral bodies, during neck flexion movements. The patient of this case was army, and he complained insidious onset of weakness and atrophy in the upper arm. Because he occurred these symptoms following hard military work, we initially suspected the possibility of traumatic brachial plexopathy. Through electrodiagnostic study, brachial plexus, cervical spine MRI, we reported this rare case of Hirayama disease with bilateral and proximal arm muscle involvement.