A Miserable Case of Eggshell Calcification of Renal Cell Carcinoma in Continuous Ambulatory Peritoneal Dialysis Patient with Sclerosing Encapsulating Peritonitis

초록

Acquired cystic kidney disease (ACKD), a common complication in patients with endstage renal disease, is characterized by more than three kidney cysts and normal or decreased sizes of both kidneys without any familial history of cystic kidney disease. In autosomal dominant polycystic kidney disease (ADPKD), however, both kidneys are usually enlarged. Extrarenal manifestations are common in ADPKD, including hepatic cysts, seminal vesicle cysts, mitral valve prolapse. A 40-year-old man presented to our emergency clinic with severe abdominal pain, nausea, and vomiting for 3 days. He had been undergoing continuous ambulatory peritoneal dialysis (CAPD) for 15 years, but it was recently changed to hemodialysis owing to sclerosing encapsulating peritonitis (SEP). Radiologic imaging studies revealed bilateral enlarged kidneys with multiple eggshell calcifi ed cysts and some hepatic cysts, which suggested ADPKD. He underwent right nephrectomy, and pathological tests revealed ACKD-associated renal cell carcinoma (RCC) confi ned to the resected kidney. He was treated with steroids for SEP, and the symptoms resolved. We herein report a rare case of ACKD―resembling ADPKD―that progressed to RCC in a patient with concurrent SEP who had been undergoing CAPD for 15 years.